Hirschsprung Disease in Brief: Presentation, Workup, Diagnosis, and Perioperative Considerations

The surgical management for Hirschsprung disease has changed dramatically over the past few decades. So here, we discuss the basics of workup, diagnosis, and surgical treatment for aganglionic megacolon AKA Hirschsprung disease with Dr. Aaron Garrison and Dr. Jason Frischer from Cincinnati Children’s Hospital Medical Center.

Hosted by Dr. Rod Gerardo, Dr. Ellen Encisco, and Dr. Todd Ponsky

CCHMD HAEC resource: https://staycurrentapp.app.link/62V0jx2Dxkb

Download the StayCurrent: Pediatric Surgery app here: https://apps.apple.com/us/app/staycurrent-pediatric-surgery/id1254498901

00:00 Introduction
01:03 Presentation of Hirschsprung disease
01:30 Incidence of Hirschsprung disease
01:43 Risk factors for developing Hirschsprung disease
02:18 Work up for Hirschsprung disease
02:42 Contrast enema
03:50 Rectal biopsy
04:30 Obtaining the rectal biopsy
05:20 Anorectal manometry
06:07 Patient/family education
06:30 Initial management of Hirschsprung disease in the NICU
07:03 Treating older patients with Hirschsprung disease
07:29 The Goals of surgical management
07:52 Options for surgical approach
08:16 Swenson, Soave, and Duhamel procedures
08:48 Post operative complications
09:14 Hirschsprung disease associated enterocolitis
10:00 Long term prognosis
10:26 Outro